Precision medicine for heritable thoracic aortic disease

Montalcino Aortic Consortium: Precision Medicine for Heritable Thoracic Aortic Disease

The University of Texas Health Science Center, Houston · NCT04005976

This study is trying to learn more about genetic factors in people with heritable thoracic aortic disease to help doctors better predict risks and manage their care.

Quick facts

Study typeObservational
Enrollment5000 (estimated)
SexAll
SponsorThe University of Texas Health Science Center, Houston (other)
Locations20 sites (Newport Beach, California and 19 other locations)
Trial IDNCT04005976 on ClinicalTrials.gov

What this trial studies

The Montalcino Aortic Consortium aims to gather large cohorts of patients with mutations in known heritable thoracic aortic disease (H-TAD) genes to better understand the associated phenotypes and identify genetic and environmental factors that influence these conditions. By employing both retrospective and prospective study designs, the consortium will characterize various stages of H-TAD and the complications linked to these genetic mutations. This comprehensive data collection will enhance the precision of risk predictions and improve clinical management for patients with genetically triggered vascular diseases.

Who should consider this trial

Good fit: Ideal candidates include patients and their relatives with confirmed pathogenic or likely pathogenic variants in specific H-TAD genes.

Not a fit: Patients without a confirmed causative variant for heritable thoracic aortic disease may not benefit from this study.

Why it matters

Potential benefit: If successful, this study could lead to improved management and outcomes for patients with heritable thoracic aortic diseases.

How similar studies have performed: Other studies focusing on genetic factors in heritable diseases have shown promise, suggesting that this approach could yield valuable insights.

Eligibility criteria

Show full inclusion / exclusion criteria
Inclusion Criteria:

* Patients and their relatives with a confirmed pathogenic, likely pathogenic variant, or variant of unknown clinical significance in at least one of the H-TAD genes (i.e. TGFBR1, TGFBR2, SMAD3, TGFB2, TGFB3, ACTA2, MYH11, MYLK, PRKG1, MAT2A, MFAP5, LOX, COL3A1, FOXE3, and FBN1).
* Patients of all ages, sex and race for which informed consent can be obtained.

Exclusion Criteria:

* Patients without a confirmed causative variant for H-TAD.

Where this trial is running

Newport Beach, California and 19 other locations

Study contacts

How to participate

  1. Review the eligibility criteria above with your treating physician.
  2. Visit the official trial page on ClinicalTrials.gov for the most current contact information and recruitment status.
  3. Contact the listed study coordinator or principal investigator to request pre-screening. Pre-screening is free and never obligates you to enroll.

View on ClinicalTrials.gov →

Conditions: Aortic Aneurysm, Aortic Dissection, Aortic Diseases

Last reviewed 2026-05-15 by the Find a Trial editorial team. Information on this page is for educational purposes and is not medical advice. Always consult qualified healthcare professionals about clinical trial participation.