Evaluating the safety of TN-201 in adults with a specific heart condition

First-in-Human, Open-Label, Safety, Tolerability, Dose-Finding, Pharmacodynamic and Cardiac Transgene Expression Study of TN-201, a Recombinant Adeno-associated Virus Serotype 9 (AAV9) Containing Myosin Binding Protein C Transgene, in Adults With MYBPC3 Mutation-associated Hypertrophic Cardiomyopathy (HCM)

Phase1; Phase2 Interventional Tenaya Therapeutics · NCT05836259

This study is testing a new gene therapy called TN-201 to see if it is safe for adults with a specific heart condition related to MYBPC3 mutations.

Quick facts

PhasePhase1; Phase2
Study typeInterventional
Enrollment30 (estimated)
Ages18 Years to 75 Years
SexAll
SponsorTenaya Therapeutics Industry-sponsored
Locations10 sites (La Jolla, California and 9 other locations)
Trial IDNCT05836259 on ClinicalTrials.gov

What this trial studies

This study is designed to assess the safety and tolerability of TN-201, a gene therapy, in adults suffering from symptomatic hypertrophic cardiomyopathy (HCM) linked to MYBPC3 mutations. It involves a single-ascending dose approach where participants will receive the active drug and be monitored for effects over a five-year period. The study will include two escalating dose cohorts and aims to enroll between 6 to 30 patients. The focus is on understanding the pharmacodynamics of TN-201 in this specific patient population.

Who should consider this trial

Good fit: Ideal candidates are adults with symptomatic hypertrophic cardiomyopathy caused by MYBPC3 mutations.

Not a fit: Patients without MYBPC3 mutations or those with high AAV9 neutralizing antibody titers may not benefit from this study.

Why it matters

Potential benefit: If successful, this treatment could provide a new therapeutic option for patients with MYBPC3 mutation-associated HCM.

How similar studies have performed: While this approach is novel, similar gene therapies have shown promise in other conditions, indicating potential for success.

Eligibility criteria

Show full inclusion / exclusion criteria
Inclusion Criteria:

* MYBPC3 mutation
* Hypertrophic Cardiomyopathy (obstructive and nonobstructive)
* Left Ventricular Ejection Fraction ≥45%
* NYHA Functional Class II or III symptoms
* NT-proBNP ≥160pg/ml

Exclusion Criteria:

* High AAV9 neutralizing antibody titer

Where this trial is running

La Jolla, California and 9 other locations

Study contacts

How to participate

  1. Review the eligibility criteria above with your treating physician.
  2. Visit the official trial page on ClinicalTrials.gov for the most current contact information and recruitment status.
  3. Contact the listed study coordinator or principal investigator to request pre-screening. Pre-screening is free and never obligates you to enroll.
Conditions Hypertrophic CardiomyopathyMyosin Binding Protein C3Nonobstructive HCMGenetic HCMFamilial HCMAdenoassociated VirusGene TherapyObstructive HCM
Last reviewed 2026-06-13 by the Find a Trial editorial team. Information on this page is for educational purposes and is not medical advice. Always consult qualified healthcare professionals about clinical trial participation.