Monitoring kidney function in cystic fibrosis patients during a treatment pause

Cystic Fibrosis in the Kidney: Monitoring the Effectiveness of Elexacaftor/tezacaftor/ivacaftor in Urine After a Short Pause of Therapy

NA · University of Aarhus · NCT05818319

This study is testing how a short break from a specific cystic fibrosis treatment affects kidney function in adults with the condition.

Quick facts

PhaseNA
Study typeInterventional
Enrollment30 (estimated)
Ages18 Years and up
SexAll
SponsorUniversity of Aarhus (other)
Locations1 site (Aarhus C, Central Jutland)
Trial IDNCT05818319 on ClinicalTrials.gov

What this trial studies

This study evaluates the impact of a short pause in treatment with the CFTR modulator combination therapy Elexacaftor/tezacaftor/ivacaftor on urine bicarbonate excretion in adult cystic fibrosis patients. The researchers aim to determine if changes in urine HCO3- excretion can serve as a biomarker for CFTR function and the effectiveness of the therapy. Participants will undergo a treatment pause of varying durations to assess these changes. The study focuses on understanding the relationship between CFTR dysfunction and kidney function in cystic fibrosis.

Who should consider this trial

Good fit: Ideal candidates are adults over 17 years with cystic fibrosis and normal kidney function.

Not a fit: Patients with critical acute illness or severe lung disease may not benefit from this study.

Why it matters

Potential benefit: If successful, this study could provide insights into kidney function in cystic fibrosis patients and improve treatment strategies.

How similar studies have performed: While the specific approach of monitoring urine HCO3- excretion in this context may be novel, related studies on CFTR modulation have shown promising results.

Eligibility criteria

Show full inclusion / exclusion criteria
Inclusion Criteria:

* Adult (age \>17 years) CF patients.
* Normal kidney function estimated by eGFR\>90.
* Adults capable of understanding and voluntarily consenting.

Exclusion Criteria:

* Critical acute illness.
* Severe lung disease (ppFEV1\<40%).
* Adults not capable of understanding and voluntarily consenting.

Where this trial is running

Aarhus C, Central Jutland

Study contacts

How to participate

  1. Review the eligibility criteria above with your treating physician.
  2. Visit the official trial page on ClinicalTrials.gov for the most current contact information and recruitment status.
  3. Contact the listed study coordinator or principal investigator to request pre-screening. Pre-screening is free and never obligates you to enroll.

View on ClinicalTrials.gov →

Conditions: Cystic Fibrosis, CFTR Gene Mutation

Last reviewed 2026-05-15 by the Find a Trial editorial team. Information on this page is for educational purposes and is not medical advice. Always consult qualified healthcare professionals about clinical trial participation.