Exploring the pulmonary blood vessels in Fontan patients

The Role of the Pulmonary Vasculature in the Fontan Circulation

University Medical Center Groningen · NCT02414321

This study looks at the blood vessels in adults who had the Fontan surgery for heart defects to see how they work during exercise and how this might help improve treatments for these patients.

Quick facts

Study typeObservational
Enrollment20 (estimated)
Ages18 Years and up
SexAll
SponsorUniversity Medical Center Groningen (other)
Locations1 site (Groningen)
Trial IDNCT02414321 on ClinicalTrials.gov

What this trial studies

This observational study investigates the structural and functional characteristics of the pulmonary vasculature in adults who have undergone the Fontan operation for congenital heart disease. It aims to determine how pulmonary vasodilatation affects cardiac output during simulated exercise and to characterize the structural properties of small pulmonary arteries. The study utilizes advanced imaging techniques like Optical Coherence Tomography and pulmonary vascular response tests to gather data during clinically indicated cardiac catheterizations. The findings may highlight the pulmonary circulation as a potential target for future treatments to improve outcomes for Fontan patients.

Who should consider this trial

Good fit: Ideal candidates include adults who have undergone the Fontan operation and have a clinical indication for cardiac catheterization.

Not a fit: Patients with significant pulmonary vascular disease or those who cannot undergo reliable cardiac index and PVR measurements may not benefit from this study.

Why it matters

Potential benefit: If successful, this study could lead to new therapeutic strategies that improve long-term outcomes for patients with Fontan circulation.

How similar studies have performed: While studies on pulmonary vascular resistance in Fontan patients exist, this specific approach using advanced imaging and vasodilators is relatively novel.

Eligibility criteria

Show full inclusion / exclusion criteria
Inclusion criteria:

Fontan group

* written informed consent
* Clinical indication for cardiac catheterization

Control group

* written informed consent
* Clinical indication for right heart catheterization
* Absence of pulmonary vascular disease
* Normal pulmonary vascular hemodynamic profile

Exclusion criteria:

Fontan group

* Standard exclusion criteria for cardiac catheterization
* Obstruction in Fontan conduit
* Inability to measure a reliable cardiac index and PVR (rhythm instability, hemodynamic or anatomic reasons)

Control Group

- No specific exclusion criteria apart from the standard exclusion criteria for right heart catheterization.

Where this trial is running

Groningen

Study contacts

How to participate

  1. Review the eligibility criteria above with your treating physician.
  2. Visit the official trial page on ClinicalTrials.gov for the most current contact information and recruitment status.
  3. Contact the listed study coordinator or principal investigator to request pre-screening. Pre-screening is free and never obligates you to enroll.

View on ClinicalTrials.gov →

Conditions: Congenital Heart Disease, Fontan Operation, Pulmonary Vascular Resistance, Pulmonary Vascular Remodeling

Last reviewed 2026-05-15 by the Find a Trial editorial team. Information on this page is for educational purposes and is not medical advice. Always consult qualified healthcare professionals about clinical trial participation.