Diagnosing frontotemporal lobar degeneration

Multimodal Assessment for Predicting Specific Pathological Substrate in Frontotemporal Lobar Degeneration

Observational University Health Network, Toronto · NCT02964637

This study is testing different ways to diagnose frontotemporal lobar degeneration to help doctors identify the condition more accurately.

Quick facts

Study typeObservational
Enrollment100 (estimated)
Ages18 Years to 90 Years
SexAll
SponsorUniversity Health Network, Toronto Academic / other
Locations1 site (Toronto, Ontario)
Trial IDNCT02964637 on ClinicalTrials.gov

What this trial studies

This study aims to establish effective diagnostic tools for accurately diagnosing frontotemporal lobar degeneration (FTLD) syndromes. It evaluates various diagnostic tests, including brain imaging, skin biopsies, body fluid samples, cognitive assessments, and everyday functioning evaluations. The findings are intended to enhance understanding of the disease mechanisms and improve diagnostic accuracy, potentially guiding future treatment strategies.

Who should consider this trial

Good fit: Ideal candidates include individuals diagnosed with specific FTLD syndromes such as behavioral variant frontotemporal dementia, progressive supranuclear palsy, and others, along with a reliable study partner.

Not a fit: Patients with conditions that can explain their symptoms, such as Alzheimer's disease or other neurological disorders, may not benefit from this study.

Why it matters

Potential benefit: If successful, this study could lead to more accurate diagnoses of frontotemporal lobar degeneration, improving patient management and treatment options.

How similar studies have performed: While this approach is focused on establishing diagnostic tools, similar studies have shown promise in improving diagnostic accuracy for neurodegenerative diseases.

Eligibility criteria

Show full inclusion / exclusion criteria
Inclusion Criteria:

* Participant must have a reliable study partner who can provide an independent evaluation of functioning.
* Able to read, understand and speak English for neuropsychological testing.
* All subjects must meet one of these diagnostic criteria (A) probable behavioral variant FTD, (B) MRI-supported non-fluent variant PPA; (C) MRI-supported semantic variant PPA and \[18F\]T807 negative (D) probable CBS: using current criteria for CBS(27); (E) PSP: inclusion criteria for PSP are based upon the National Institute of Neurological Disorders and Stroke Society of Progressive Supranuclear Palsy (NINDS-SPSP) (F) FTD-MND
* Control subjects must have a normal neurological exam, a CDR sum of boxes = 0, and MMSE score equal to or greater than 28

Exclusion Criteria:

* Patients with clinical, imaging or CSF A beta/ tau profile consistent with AD
* History of traumatic brain injury, brain tumors, stroke or other neurological or psychiatric disorders that can explain symptoms will be excluded.
* Premenopausal women will be asked to consent to a pregnancy test prior to each scan as pregnant women will be excluded from study because of potential harm to fetus from PET study.
* Presence of pacemakers, aneurysm clips, artificial heart valves, ear implants, metal fragments or foreign objects in the eyes, skin or body.

Where this trial is running

Toronto, Ontario

Study contacts

How to participate

  1. Review the eligibility criteria above with your treating physician.
  2. Visit the official trial page on ClinicalTrials.gov for the most current contact information and recruitment status.
  3. Contact the listed study coordinator or principal investigator to request pre-screening. Pre-screening is free and never obligates you to enroll.
Conditions Corticobasal SyndromeProgressive Supranuclear PalsyBehavioral Variant Frontotemporal DementiaSemantic DementiaProgressive Nonfluent AphasiaAmyotrophic Lateral Sclerosis And/or Frontotemporal Dementia
Last reviewed 2026-06-13 by the Find a Trial editorial team. Information on this page is for educational purposes and is not medical advice. Always consult qualified healthcare professionals about clinical trial participation.