Using simple sugars to improve health in children with congenital disorders of glycosylation

Dietary Monosaccharide Supplementation in Patients With Congenital Disorders of Glycosylation

Observational Mayo Clinic · NCT04198987

This study is testing if giving simple sugars every day can help improve the health of children with congenital disorders of glycosylation.

Quick facts

Study typeObservational
Enrollment100 (estimated)
SexAll
SponsorMayo Clinic Academic / other
Locations1 site (Rochester, Minnesota)
Trial IDNCT04198987 on ClinicalTrials.gov

What this trial studies

This observational study aims to evaluate the effects of daily dietary supplementation with simple sugars in children diagnosed with congenital disorders of glycosylation (CDG). Researchers will collect data from patients who are currently receiving or planning to receive these sugar supplements to assess their health outcomes. The study seeks to expand the existing evidence regarding the potential benefits of this treatment in clinical practice.

Who should consider this trial

Good fit: Ideal candidates for this study are children with a biochemically and genetically confirmed diagnosis of congenital disorders of glycosylation who are receiving or planning to receive oral simple sugar supplementation.

Not a fit: Patients with conditions such as aldolase B deficiency, galactosemia, hemolytic uremic syndrome, severe anemia, or galactose intolerance may not benefit from this study.

Why it matters

Potential benefit: If successful, this approach could lead to improved health and quality of life for children suffering from congenital disorders of glycosylation.

How similar studies have performed: While this approach is being explored, there is limited existing evidence on the effectiveness of dietary monosaccharide supplementation specifically for congenital disorders of glycosylation, making this study relatively novel.

Eligibility criteria

Show full inclusion / exclusion criteria
Inclusion Criteria:

* Patient has a biochemically and genetically proven congenital disorder of glycosylation
* Patient is receiving (or planning to receive) oral simple sugar supplementation

Exclusion Criteria:

* Aldolase B deficiency
* Galactosemia
* Hemolytic uremic syndrome
* Severe anemia
* Galactose intolerance

Where this trial is running

Rochester, Minnesota

Study contacts

How to participate

  1. Review the eligibility criteria above with your treating physician.
  2. Visit the official trial page on ClinicalTrials.gov for the most current contact information and recruitment status.
  3. Contact the listed study coordinator or principal investigator to request pre-screening. Pre-screening is free and never obligates you to enroll.
Conditions Congenital Disorder of Glycosylation
Last reviewed 2026-06-13 by the Find a Trial editorial team. Information on this page is for educational purposes and is not medical advice. Always consult qualified healthcare professionals about clinical trial participation.