Research on therapeutic targets for nephronophthisis and related kidney diseases

Research of Therapeutic Targets in the Frame of Nephronophthisis and Renal Associated Ciliopathies - NPH_1

Not applicable Interventional Imagine Institute · NCT06648044

This study is trying to find new treatment options for nephronophthisis and related kidney diseases by testing if existing drugs can fix problems in cells affected by this genetic condition.

Quick facts

PhaseNot applicable
Study typeInterventional
Enrollment310 (estimated)
SexAll
SponsorImagine Institute Academic / other
Locations1 site (La Defense)
Trial IDNCT06648044 on ClinicalTrials.gov

What this trial studies

This study focuses on nephronophthisis (NPH), a genetically heterogeneous kidney disease caused by mutations in over 20 genes. It aims to investigate the therapeutic targets associated with NPH and renal ciliopathies by studying NPHP proteins and their signaling pathways. The research will explore the potential of approved drugs to correct ciliary and epithelial defects in cells with NPHP mutations. The study includes affected patients, their healthy relatives, and control patients to better understand the disease and its treatment options.

Who should consider this trial

Good fit: Ideal candidates include patients diagnosed with nephronophthisis or renal associated ciliopathies, as well as their healthy relatives.

Not a fit: Patients with chronic renal diseases unrelated to nephronophthisis may not benefit from this study.

Why it matters

Potential benefit: If successful, this research could lead to effective treatments for nephronophthisis and improve outcomes for affected patients.

How similar studies have performed: While there is ongoing research in this area, the specific approach of targeting NPHP proteins and their signaling pathways is relatively novel.

Eligibility criteria

Show full inclusion / exclusion criteria
Inclusion Criteria:

* In order to be included in the protocol, subjects will have to respect the following criteria:

Affected patients:

Suffering from nephronophthisis or renal associated ciliopathies with known genetic diagnosis or not, Having obtained the signature of the informed consent form of patient, parent(s) or legal representative No age limit is requested for these patients, who can be recruited from birth.

Healthy relatives:

Being the healthy relative (father / mother / brother / sister) of an included patient Having signed the informed consent form (patient or parent in case of minor subject) No age limit is requested for these subjects, who can be recruited from birth.

'Negative' control patients: Being unscathed of any chronic renal disease, with or without ciliopathies Having obtained the signature of the informed consent form No age limit is requested for these patients, who can be recruited from birth.

'Positive' control patients Suffering from Chronic Kidney Disease unrelated to ciliary dysfunction (such as glomerulopathy, tubulopathy…) Having obtained the signature of the informed consent form No age limit is requested for these patients, who can be recruited from birth.

Exclusion Criteria:

In order to be included in the protocol, subjects will have to fulfill none of the following criteria:

Affected patients:

Patients with a functioning kidney transplant (only for patient for who urine sample is performed. This criteria is not applicable when only blood is sampling) Patients included in a therapeutic protocol since fewer 30 days.

Healthy relatives:

No no-inclusion criteria

'Negative' control subjects: No no-inclusion criteria

'Positive' control subjects: Patients with a functioning kidney transplant

Where this trial is running

La Defense

How to participate

  1. Review the eligibility criteria above with your treating physician.
  2. Visit the official trial page on ClinicalTrials.gov for the most current contact information and recruitment status.
  3. Contact the listed study coordinator or principal investigator to request pre-screening. Pre-screening is free and never obligates you to enroll.
Conditions NephronophthisisNPH1AutosomalRecessiveGeneticallyHeterogenicDisordermutations
Last reviewed 2026-06-13 by the Find a Trial editorial team. Information on this page is for educational purposes and is not medical advice. Always consult qualified healthcare professionals about clinical trial participation.