Registry for Epithelioid Hemangioendothelioma

The Observational EURACAN Prospective Clinical Registry Dedicated to Epithelioid Hemangioendothelioma: the Protocol of an International and Collaborative Effort on an Ultra-rare Entity

Observational Fondazione IRCCS Istituto Nazionale dei Tumori, Milano · NCT06408441

This study is collecting information from people newly diagnosed with epithelioid hemangioendothelioma to better understand the disease and how it’s treated.

Quick facts

Study typeObservational
Enrollment100 (estimated)
Ages18 Years and up
SexAll
SponsorFondazione IRCCS Istituto Nazionale dei Tumori, Milano Academic / other
Drugs / interventionschemotherapy, radiation
Locations22 sites (Graz, Graz and 21 other locations)
Trial IDNCT06408441 on ClinicalTrials.gov

What this trial studies

This registry collects high-quality prospective data on patients diagnosed with epithelioid hemangioendothelioma (EHE), an ultra-rare sarcoma. The study aims to improve understanding of the disease's natural history, identify prognostic factors, and evaluate treatment patterns and efficacy. It includes only new cases confirmed by expert pathologists and focuses on gathering comprehensive clinical data to address existing knowledge gaps. The registry is part of the European Reference Network on Rare Adult Solid Cancers (EURACAN).

Who should consider this trial

Good fit: Ideal candidates are adult patients aged 18 years and older with a newly diagnosed, pathologically confirmed case of EHE.

Not a fit: Patients with a diagnosis of EHE prior to December 1, 2023, or those without molecular confirmation of the diagnosis will not benefit from this study.

Why it matters

Potential benefit: If successful, this registry could lead to improved management and treatment strategies for patients with epithelioid hemangioendothelioma.

How similar studies have performed: While this registry approach is novel for EHE, similar registries for rare cancers have shown success in improving understanding and treatment outcomes.

Eligibility criteria

Show full inclusion / exclusion criteria
Inclusion Criteria:

* New patients managed by the contributing centers with a pathological EHE diagnosis performed or verified by an expert sarcoma pathologist starting from 1 December 2023 onwards and to be performed within 6 months from the registration
* Molecular confirmation of the diagnosis (WWTR1-CAMTA1 or YAP1-TFE3)
* Adult patients (aged ≥ 18 years)

Where this trial is running

Graz, Graz and 21 other locations

Study contacts

How to participate

  1. Review the eligibility criteria above with your treating physician.
  2. Visit the official trial page on ClinicalTrials.gov for the most current contact information and recruitment status.
  3. Contact the listed study coordinator or principal investigator to request pre-screening. Pre-screening is free and never obligates you to enroll.
Conditions Epithelioid HemangioendotheliomaSarcoma,Soft Tissuerare cancerssoft tissue rare cancerregistryprotocolultra rare sarcomas
Last reviewed 2026-06-13 by the Find a Trial editorial team. Information on this page is for educational purposes and is not medical advice. Always consult qualified healthcare professionals about clinical trial participation.