Observing the clinical course of homocystinuria caused by CBS deficiency

A Multicenter, Observational, Prospective, Natural History Study of Homocystinuria Due to Cystathionine Beta-synthase Deficiency in Pediatric and Adult Patients (ACAPPELLA)

Observational Travere Therapeutics, Inc. · NCT02998710

This study looks at how homocystinuria affects people aged 1 to 65 who are already receiving treatment to better understand the condition over time.

Quick facts

Study typeObservational
Enrollment150 (estimated)
Ages1 Year to 65 Years
SexAll
SponsorTravere Therapeutics, Inc. Industry-sponsored
Locations11 sites (Culver City, California and 10 other locations)
Trial IDNCT02998710 on ClinicalTrials.gov

What this trial studies

This observational study aims to characterize the clinical course of homocystinuria in patients aged 1 to 65 years who are currently receiving clinical management. It will involve collecting data on the health status and treatment outcomes of individuals diagnosed with homocystinuria due to cystathionine beta-synthase deficiency. The study will not involve any experimental treatments but will focus on understanding the natural history of the condition under existing management practices.

Who should consider this trial

Good fit: Ideal candidates include males and females aged 1 to 65 years who have been clinically diagnosed with homocystinuria.

Not a fit: Patients with significant postnatal complications or congenital anomalies unrelated to homocystinuria may not benefit from this study.

Why it matters

Potential benefit: If successful, this study could provide valuable insights into the progression of homocystinuria, potentially leading to improved management strategies for patients.

How similar studies have performed: While this study focuses on the natural history of a specific condition, similar observational studies have provided critical insights into other metabolic disorders, suggesting potential for meaningful findings.

Eligibility criteria

Show full inclusion / exclusion criteria
Inclusion Criteria:

* Patients who are clinically diagnosed with homocystinuria
* Male/female patients aged 1 to 65 years
* Patients who consented and/or assented
* Patients who are willing and able to comply with all study-related procedures.

Exclusion Criteria:

* Medically significant postnatal complications or congenital anomalies that are not associated with homocystinuria
* Received any experimental therapy for homocystinuria during the 6 months prior to enrollment or expected to receive any such therapy during duration of the study

Where this trial is running

Culver City, California and 10 other locations

Study contacts

How to participate

  1. Review the eligibility criteria above with your treating physician.
  2. Visit the official trial page on ClinicalTrials.gov for the most current contact information and recruitment status.
  3. Contact the listed study coordinator or principal investigator to request pre-screening. Pre-screening is free and never obligates you to enroll.
Conditions Homocystinuria Due to CBS Deficiency
Last reviewed 2026-06-13 by the Find a Trial editorial team. Information on this page is for educational purposes and is not medical advice. Always consult qualified healthcare professionals about clinical trial participation.