Long-term follow-up of Korean CADASIL patients

Long-term Prognosis of Korean Cerebral Autosomal Dominant Arteriopathy With Subcortical Infarcts and Leukoencephalopathy(CADASIL) Patients: A Multicenter Prospective Study

Observational Jeju National University Hospital · NCT07497867

This 10-year project will track symptoms, brain scans, cognitive tests, and genetic data in about 500 Korean adults with CADASIL to see how the disease progresses.

Quick facts

Study typeObservational
Enrollment500 (estimated)
Ages19 Years and up
SexAll
SponsorJeju National University Hospital Academic / other
Locations1 site (Jeju City, Jeju-do)
Trial IDNCT07497867 on ClinicalTrials.gov

What this trial studies

K-CADASIL is a nationwide, multicenter prospective cohort that will enroll roughly 500 Korean adults with suspected or genetically confirmed CADASIL and follow them for 10 years. Participants will undergo regular clinic visits with neurological exams, MRI brain imaging, blood sampling, and standardized neuropsychological testing. Collected samples and data will form a genomic and proteomic biorepository to enable future multi-omics analyses. The program aims to link clinical features, imaging changes, comorbidities, and molecular markers to long-term outcomes in this population.

Who should consider this trial

Good fit: Adults (age 19 or older) in Korea with suspected or confirmed NOTCH3-related CADASIL who can provide informed consent are the intended participants.

Not a fit: People who cannot undergo MRI (for example due to pacemakers, metal implants, or severe claustrophobia) or who had an acute stroke within the last 180 days are likely to be excluded and may not benefit from participation.

Why it matters

Potential benefit: If successful, this work could improve predictions of disease course and help tailor monitoring and care for Korean patients with CADASIL.

How similar studies have performed: Large cohorts in Europe have described CADASIL natural history and genotype-phenotype links, but a long-term, multicenter Korean cohort of this size is novel.

Eligibility criteria

Show full inclusion / exclusion criteria
Inclusion Criteria:

* Age ≥ 19 years
* CADASIL suspected or confirmed by genetic testing (NOTCH3 mutation)
* Able to provide written informed consent (participant or legally authorized representative)

Exclusion Criteria:

* Contraindication to MRI (claustrophobia, metal implants, pacemaker)
* Acute ischemic or hemorrhagic stroke within 180 days prior to enrollment

Where this trial is running

Jeju City, Jeju-do

Study contacts

How to participate

  1. Review the eligibility criteria above with your treating physician.
  2. Visit the official trial page on ClinicalTrials.gov for the most current contact information and recruitment status.
  3. Contact the listed study coordinator or principal investigator to request pre-screening. Pre-screening is free and never obligates you to enroll.
Conditions CADASILCerebral Autosomal Dominant Arteriopatie With Subcortical Infarcts and LeukoencephalopathyNOTCH3StrokeCerebral Small Vessel DiseaseProspective StudyKorea
Last reviewed 2026-06-13 by the Find a Trial editorial team. Information on this page is for educational purposes and is not medical advice. Always consult qualified healthcare professionals about clinical trial participation.