Gene therapy for children with limb girdle muscular dystrophy type 2c

A Phase 1-2, Open-label, Dose Escalation Study to Evaluate the Safety of 2 Doses of Intravenous ATA-200, an Adeno-associated Viral Vector Carrying the Human SGCG Gene, in Patients with Gamma-sarcoglycanopathy (LGMDR5)

Phase1; Phase2 Interventional Atamyo Therapeutics · NCT05973630

This study is testing a new gene therapy to see if it can safely help children with limb girdle muscular dystrophy type 2c improve their condition.

Quick facts

PhasePhase1; Phase2
Study typeInterventional
Enrollment6 (estimated)
Ages6 Years to 13 Years
SexAll
SponsorAtamyo Therapeutics Industry-sponsored
Locations3 sites (Gainsville, Florida and 2 other locations)
Trial IDNCT05973630 on ClinicalTrials.gov

What this trial studies

This clinical trial evaluates the safety and tolerability of a single intravenous infusion of ATA-200 in pediatric patients diagnosed with limb girdle muscular dystrophy type 2c (LGMDR5). The trial is designed as a multicenter Phase 1b study, where patients will be treated in two sequential dose cohorts. The first cohort will consist of three patients receiving a potentially effective dose, followed by a second cohort with a higher dose after safety data review. Participants will be monitored for safety and efficacy over a period of 4.5 years following treatment.

Who should consider this trial

Good fit: Ideal candidates are ambulant children aged 6 to less than 12 years with a confirmed diagnosis of LGMDR5.

Not a fit: Patients with detectable neutralizing antibodies against AAV8 or significant comorbid conditions may not benefit from this study.

Why it matters

Potential benefit: If successful, this therapy could provide a new treatment option for children suffering from LGMDR5, potentially improving their mobility and quality of life.

How similar studies have performed: While gene therapy approaches for muscular dystrophies are being explored, this specific trial represents a novel application targeting LGMDR5.

Eligibility criteria

Show full inclusion / exclusion criteria
Inclusion Criteria:

* Confirmed diagnosis of LGMDR5 before age of 10, based on clinical presentation and genotyping
* Ambulant male or female patients aged 6 to less than 12 years of age at screening
* Able to perform the 10-meter walk test (10MWT) in less than 15 sec and to rise from chair with or without arm support

Exclusion Criteria:

* Detectable neutralizing antibodies against AAV8
* Cardiomyopathy with left ventricular ejection fraction (LVEF) \< 50%
* Respiratory assistance
* Concomitant medical condition that might interfere with LGMDR5 evolution
* Acute illness within 4 weeks of anticipated IMP administration
* Current participation in another clinical trial with investigational medicinal product
* Previous participation in gene and cell therapy trials
* Any condition that would contraindicate immunosuppressant treatment
* Presence of any permanent items (e.g., metal braces) precluding undergoing MRI
* Any vaccination 1 month prior to planned IMP administration
* Serology consistent with HIV exposure or active hepatitis B or C infection
* Grade 2 or higher lab abnormalities for liver function tests, creatinine, hemogram and coagulation

Where this trial is running

Gainsville, Florida and 2 other locations

Study contacts

How to participate

  1. Review the eligibility criteria above with your treating physician.
  2. Visit the official trial page on ClinicalTrials.gov for the most current contact information and recruitment status.
  3. Contact the listed study coordinator or principal investigator to request pre-screening. Pre-screening is free and never obligates you to enroll.
Conditions LGMD2C
Last reviewed 2026-06-13 by the Find a Trial editorial team. Information on this page is for educational purposes and is not medical advice. Always consult qualified healthcare professionals about clinical trial participation.