Combining mirdametinib and vorinostat for treating specific nerve tumors in NF1 patients

A Window of Opportunity Trial of Mirdametinib Plus Vorinostat for NF1 Associated, H3K27 Trimethylation Deficient Malignant Peripheral Nerve Sheath Tumor [MPNST]

Early Phase 1 Interventional University of Minnesota · NCT06693284

This study is testing a new combination of two medications to see if they can help patients with a specific type of nerve tumor related to Neurofibromatosis type 1 before starting regular treatments.

Quick facts

PhaseEarly Phase 1
Study typeInterventional
Enrollment8 (estimated)
Ages12 Years and up
SexAll
SponsorUniversity of Minnesota Academic / other
Drugs / interventionsmirdametinib, chemotherapy, Radiation
Locations1 site (Minneapolis, Minnesota)
Trial IDNCT06693284 on ClinicalTrials.gov

What this trial studies

This trial investigates the effectiveness of a short course of mirdametinib and vorinostat in patients with newly diagnosed malignant peripheral nerve sheath tumors (MPNSTs) associated with Neurofibromatosis type 1 (NF1) and specific histone deficiencies. The study aims to enroll 4 to 8 patients aged 12 years or older who meet the biomarker criteria. Participants will undergo imaging and a biopsy before receiving the treatment, followed by a repeat MRI to assess the tumor's response. This early-phase trial serves as a 'window of opportunity' before standard treatment options are initiated.

Who should consider this trial

Good fit: Ideal candidates are individuals aged 12 years or older with NF1 and histone H3K27 trimethylation deficient MPNST.

Not a fit: Patients without NF1 or those with other types of tumors not meeting the histone deficiency criteria may not benefit from this study.

Why it matters

Potential benefit: If successful, this approach could provide a new treatment option for patients with aggressive nerve tumors, potentially improving outcomes.

How similar studies have performed: While this specific combination is novel, similar approaches targeting tumor biology in NF1-related tumors have shown promise in other studies.

Eligibility criteria

Show full inclusion / exclusion criteria
Inclusion Criteria:

* Known Neurofibromatosis type 1 (NF-1) syndrome based on current diagnostic criteria.
* Diagnosis of suspected MPNST by PET or MRI imaging
* Confirmation of histone H3 lysine 27 trimethylation-negative MPSNT by immunohistochemistry
* Twelve years of age or older
* Complete blood count (CBC), platelet, liver and kidney function within institutional normal limits performed within 14 days of 1 st dose of study drug.
* Must be able to swallow capsules.
* Females of childbearing potential must use highly effective contraception (see inclusion criteria section) from the time of study enrollment through 6 months after the last dose of vorinostat and mirdametinib. Males with partners of childbearing potential must use highly effective contraception from the time of study enrollment through 3 months after the last dose of vorinostat.
* Provides voluntary written consent prior to any study related activities, with parental/guardian consent and assent for those 12 to 17 years of age at enrollment.

Exclusion Criteria:

* Pregnant or breastfeeding - females of childbearing potential must have a negative pregnancy test (serum or urine) within 7 days prior to the 1 st dose of the study drugs.
* Significant cardiac disease
* Significant eye disease
* Radiation therapy or chemotherapy in the past year.

Where this trial is running

Minneapolis, Minnesota

Study contacts

How to participate

  1. Review the eligibility criteria above with your treating physician.
  2. Visit the official trial page on ClinicalTrials.gov for the most current contact information and recruitment status.
  3. Contact the listed study coordinator or principal investigator to request pre-screening. Pre-screening is free and never obligates you to enroll.
Conditions Primary Malignant Peripheral Nerve Sheath Tumors
Last reviewed 2026-06-13 by the Find a Trial editorial team. Information on this page is for educational purposes and is not medical advice. Always consult qualified healthcare professionals about clinical trial participation.