Understanding how gene changes cause childhood brain cancer

Developmental transcription factors in Drosha-driven cancer

NIH-funded research Ut Southwestern Medical Center · NIH-11176811

This research aims to understand how specific gene mutations lead to pineoblastoma, a type of childhood brain cancer, to find new ways to treat it.

Quick facts

Grant typeR01 grant
Study typeNIH-funded research
Funding institutionUt Southwestern Medical Center NIH-funded
Lab location1 site (Dallas, United States)
Project IDNIH-11176811 on NIH RePORTER

What this research studies

Pineoblastoma is a childhood brain cancer caused by changes in genes called DROSHA and DICER1, but we don't fully understand how these changes lead to cancer or how to treat them. Our team has created a special mouse model that develops tumors similar to human pineoblastoma to learn more. We've found that certain developmental genes are overactive in these tumors, and we want to see if one of these genes, called Onecut2, is essential for the cancer to grow. By studying how Onecut2 works with other genes and testing its role in patient-derived tumor models, we hope to uncover new treatment possibilities.

Who could benefit from this research

Good fit: This foundational research could eventually benefit children diagnosed with pineoblastoma, especially those with DROSHA or DICER1 gene mutations.

Not a fit: Patients with other types of brain cancer not linked to DROSHA or DICER1 mutations may not directly benefit from this specific research.

Why it matters

Potential benefit: If successful, this work could identify new targets for therapies that specifically treat pineoblastoma caused by DROSHA or DICER1 mutations.

How similar studies have performed: The specific pathways by which these mutations cause cancer are not fully understood, and there are currently no targeted therapies for these mutations, making this a novel approach.

Where this research is happening

Dallas, United States

Researchers

About this research

  1. This is an active NIH-funded research project — typically early-stage science, not a clinical trial accepting patient enrollment.
  2. Some NIH-funded labs run parallel clinical studies or seek volunteers for related work. To check, contact the principal investigator or institution listed above.
  3. For full project details, budget, and progress reports, visit the official NIH RePORTER page below.
Last reviewed 2026-06-13 by the Find a Trial editorial team. Information on this page is for educational purposes and is not medical advice. Always consult qualified healthcare professionals about clinical trial participation.