Understanding genetic factors affecting heart defects in a specific genetic syndrome

Genetic modifiers of congenital heart disease in 22q11.2 deletion syndrome

NIH-funded research Albert Einstein College of Medicine · NIH-11023067

This study is looking at how genes might affect heart problems in kids with 22q11.2 deletion syndrome, which happens in about 1 in 4000 births, to help understand why some kids have more serious heart issues than others.

Quick facts

Grant typeR01 grant
Study typeNIH-funded research
Funding institutionAlbert Einstein College of Medicine NIH-funded
Lab location1 site (Bronx, United States)
Project IDNIH-11023067 on NIH RePORTER

What this research studies

This research investigates the genetic factors that influence congenital heart disease (CHD) in patients with 22q11.2 deletion syndrome, a condition that affects 1 in 4000 live births. By analyzing genetic data from both human subjects and animal models, the study aims to identify genetic modifiers that contribute to the variability in heart defects observed in these patients. Approximately 60% of individuals with this syndrome experience heart issues, which can range from mild to severe, often requiring surgical intervention. The research utilizes whole genome sequencing to explore the genetic landscape and its impact on heart development.

Who could benefit from this research

Good fit: Ideal candidates for this research are individuals diagnosed with 22q11.2 deletion syndrome, particularly those experiencing congenital heart disease.

Not a fit: Patients without 22q11.2 deletion syndrome or those who do not have congenital heart defects may not benefit from this research.

Why it matters

Potential benefit: If successful, this research could lead to improved understanding and management of congenital heart defects in patients with 22q11.2 deletion syndrome.

How similar studies have performed: Previous research has successfully identified genetic modifiers in other congenital conditions, suggesting potential for similar breakthroughs in this area.

Where this research is happening

Bronx, United States

Researchers

About this research

  1. This is an active NIH-funded research project — typically early-stage science, not a clinical trial accepting patient enrollment.
  2. Some NIH-funded labs run parallel clinical studies or seek volunteers for related work. To check, contact the principal investigator or institution listed above.
  3. For full project details, budget, and progress reports, visit the official NIH RePORTER page below.
Conditions 22q11 Chromosomal Microdeletion Syndrome22q11 Deletion Syndrome22q11.2 deletion syndrome
Last reviewed 2026-06-13 by the Find a Trial editorial team. Information on this page is for educational purposes and is not medical advice. Always consult qualified healthcare professionals about clinical trial participation.