Investigating how mutations in mitochondrial DNA affect health and aging

Functional Characterization of Mitochondrial Genome Nonsense Mutations

NIH-funded research Johns Hopkins University · NIH-11058499

This study is looking at how certain changes in our mitochondrial DNA might affect our health and how we age, especially in relation to heart cells, and it's for anyone interested in understanding the links between these DNA changes and diseases that come with getting older.

Quick facts

Grant typeR21 grant
Study typeNIH-funded research
Funding institutionJohns Hopkins University NIH-funded
Lab location1 site (Baltimore, United States)
Project IDNIH-11058499 on NIH RePORTER

What this research studies

This research focuses on understanding the role of mitochondrial DNA mutations, particularly nonsense mutations, in human health and aging. By analyzing data from approximately 200,000 samples in the UK Biobank, the study aims to explore how these mutations contribute to increased mortality risk and their impact on cellular functions such as energy metabolism and cell signaling. The researchers will use advanced techniques like base editing to manipulate mitochondrial DNA and assess the effects on heart cell activity. This approach could provide insights into the mechanisms linking mitochondrial mutations to aging-related diseases.

Who could benefit from this research

Good fit: Ideal candidates for this research include individuals with a family history of aging-related diseases or those exhibiting symptoms associated with mitochondrial dysfunction.

Not a fit: Patients with no known mitochondrial issues or those not experiencing aging-related diseases may not benefit from this research.

Why it matters

Potential benefit: If successful, this research could lead to new strategies for preventing or treating aging-related diseases linked to mitochondrial dysfunction.

How similar studies have performed: Previous research has shown that targeting mitochondrial mutations can lead to significant improvements in understanding and potentially treating related health issues, indicating a promising avenue for further exploration.

Where this research is happening

Baltimore, United States

Researchers

About this research

  1. This is an active NIH-funded research project — typically early-stage science, not a clinical trial accepting patient enrollment.
  2. Some NIH-funded labs run parallel clinical studies or seek volunteers for related work. To check, contact the principal investigator or institution listed above.
  3. For full project details, budget, and progress reports, visit the official NIH RePORTER page below.
Conditions aging associated diseaseaging associated disordersaging related diseaseaging related disorders
Last reviewed 2026-06-13 by the Find a Trial editorial team. Information on this page is for educational purposes and is not medical advice. Always consult qualified healthcare professionals about clinical trial participation.